

4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt by Molecular Depot is a 4-methylumbelliferyl-α-L-iduronic acid cyclohexylammonium salt, a fluorogenic substrate for α-L-iduronidase. α-L-Iduronidase removes iduronic acid from dermatan and heparan sulfate, and its deficiency causes mucopolysaccharidosis type I, the Hurler and Scheie syndromes. It is used as a substrate in fluorometric α-L-iduronidase assays, in mucopolysaccharidosis type I enzyme testing and in enzyme activity screening. Each unit contains 1 mg. MBP supplies Molecular Depot research reagents to research labs in the United States, Canada and worldwide.